Chapter 130 Notice
The three words "catastrophic" in the name of catastrophic antiphospholipid syndrome have clearly shown the power of this disease - catastrophic. Compared with ordinary antiphospholipid syndrome, the incidence characteristics of catastrophic antiphospholipid syndrome are not very similar. Generally, antiphospholipid syndrome is mainly dominated by large blood vessel thrombosis, the disease progresses slowly, and generally does not involve multiple organs.
But catastrophic antiphospholipid syndrome is completely different. It is a serious disease with a clinical mortality rate of more than 50%. It involves more than three organs within one week of onset, and contains arterial venous thrombosis, and microvascular thrombosis is the main manifestation. Most patients eventually die from DIC symptoms caused by pulmonary embolism or abnormal coagulation.
The most terrifying thing is that there is no ideal treatment for catastrophic antiphospholipid syndrome.
"If it's CAPS, it's bad." Yuan Ping'an's face was as deep as iron. He told Sun Lien, "The patient had just received thrombolytic anticoagulation treatment, but his small intestine ischemic necrosis has not been completely reversed. If the necrosis area continues to expand, he has to risk the intraoperative heavy bleeding."
"This risk is completely acceptable than the risk of small intestinal necrosis." Dr. Pascal is not worried about this. "First do an APL antibody test. Confirm CAPS, then start hormone shock and immunosuppression treatment immediately, and supplemented with plasma replacement. This way, antibody aggregation can be controlled in the shortest time and reduce the risk of abnormal coagulation in the case of deheparinization. As long as the plasma replacement is timely enough, he should be able to undergo surgical treatment safely."
The treatment plan proposed by Dr. Pascal is a standard response method. For the current situation, this is the only thing doctors can do for Xia Hongyuan.
"Let's notice for serious illness." Sun Lien sighed. He really didn't want to see this situation. A teacher who is loved by students, a young and energetic first-level athlete, is now lying in the rescue room dying. Even if he has undergone surgery, has removed the blood clot and undergoes thrombolysis treatment, his chance of survival is still half and half.
How could Sun Lien be relaxed in this situation?
"I'll go talk to my family." Seeing Yuan Ping'an bringing the seriously ill notice, Sun Lien stood up and took the notice, and turned to Dr. Pascal and said, "After the family agree, start treatment immediately."
Sun Lien left the most difficult work to himself.
Xia Hongyuan's parents waited outside the door for four hours. Their only child had undergone an operation, but when they saw the doctors as if they were facing a great enemy, Xia Hongyuan's parents couldn't figure out why the doctor was so nervous. After the operation, shouldn't the child get better gradually?
"Doctor Sun!" Xia Hongyuan's father saw Sun Lien from afar. He quickly stood up, walked forward and asked, "How is his condition?"
Sun Lien looked around with some embarrassment. This was the rescue hall and there were many people nearby. He whispered, "He is in a stable situation now. Please come with me first. This is not a place to talk about things."
Xia Hongyuan's father suddenly felt a slump in his heart. He tried hard to hold his wife's hand. But the irresistible tremor in his body could be seen as long as he was not blind.
Sun Lien sighed softly and took the two of them to the small conference room.
Dr. Pascal originally thought that Sun Lien would take the parents to other conference rooms, but he didn't expect that he brought the person here directly. Looking at the middle-aged couple on the opposite side, Dr. Pascal also sighed. He stood up and found two paper cups, poured some tea into it.
"Please sit down, these are colleagues from our treatment group." Sun Lien asked the two to sit down, and then handed over the notice of serious illness that they had been holding. "Please sign this notice of serious illness."
A large pile of water suddenly appeared in the water cup that Xia Hongyuan's father had just picked up, "What's going on?"
Sun Lien sighed again. "Just as you two know, we have already had surgery for Xia Hongyuan. But his problem is not just the part that our surgery can solve." He pointed to the whiteboard full of the order of symptoms. "Xia Hongyuan's disease caused all these symptoms, and based on the information we have so far, we believe that the name of this disease is called 'catastrophic antiphospholipid syndrome'."
"You mean...you are not completely sure yet?" Xia Hongyuan's father keenly noticed the problem in this statement.
"We are still waiting for the final decisive evidence to examine it." Sun Lien replied, "but according to the current situation, the possibility of this disease is the greatest."
Xia Hongyuan's father was silent for a moment and asked, "If it is this disease, how should we treat it?"
"Let me explain this part." Sun Lien was about to speak, but Dr. Pascal stood up by himself. "This is my professional content."
"I am a doctor in the Department of Rheumatology and Immunology, Pascal." Dr. Pascal briefly introduced the parents. "According to our diagnosis, the disease Xia Hongyuan suffered from is a relatively rare autoimmune disease, and the main feature of this disease is abnormal coagulation in the blood vessels of the body."
"First of all, we still cannot determine the cause of this disease. However, according to research, trauma may be the main factor causing this serious reaction. But considering his previous experience as a professional athlete, we cannot narrow the scope to which specific trauma." Dr. Pascal's voice was very calm, and it sounded slower than he usually spoke. "But his disease was very hidden, and there were not many organs involved at the beginning." He pointed to the content on the whiteboard, "The first organ to be involved should be the small intestine." Dr. Pascal looked at Xia Hongyuan's mother who was already crying with some sympathy. "That is, when you received a call from him saying that your stomach was uncomfortable."
"And later, he was sent to the hospital and had a severe pain all over his body. At present, we believe it was caused by a blood clot in his brain." Dr. Pascal continued, "This blood clot should not be big, so he did not show severe stroke symptoms, but showed unexplained pain."
"After entering the hospital, we first relieved his pain symptoms." The next part was what Xia Hongyuan's parents knew, but Dr. Pascal's explanation was still very detailed. "And we recalled Dr. Sun immediately." He pointed to Sun Lien, who was listening carefully, and praised him a few words, "He is the leader of our treatment group and the doctor with the best diagnosis skills."
Of course, Lao Pa’s flattery is not to flatter Sun Lien, but to a little relieve the emotions of the two of them. After learning that the doctor who treats his children with high standards can indeed relieve the pressure on many patients’ families.
"After multiple tests, we gradually locked his disease on the current 'CAPS'." Dr. Pascal said a lot in the middle, and then continued, "Because we have issued a notice of serious illness to you, considering the degree of danger of this disease."
The rest of the content is Sun Lien, "First of all, I will tell you that Xia Hongyuan's disease is very dangerous."
Chapter completed!